Incontinentia Pigmenti

IP

Incontinentia Pigmenti (IP) is a genetic disorder that affects the skin, hair, teeth, and nails. It is also known as Bloch Sulzberger syndrome, Bloch Siemens syndrome, melanoblastosis cutis and naevus pigmentosus systematicus. The skin lesions evolve through characteristic stages: blistering (from birth to about four months of age), a wart-like rash (for several months), swirling macular hyperpigmentation (from about six months of age into adulthood), followed by linear hypopigmentation. A ...