Jervell and Lange-Nielsen syndrome

Cardio-auditory-syncope syndrome; Cardioauditory syndrome of Jervell and Lange-Nielsen; JLNS; Surdo-cardiac syndrome

Jervell and Lange-Nielsen syndrome is a condition that causes profound hearing loss and arrhythmia, it is a type of long QT syndrome. This condition is inherited in an autosomal recessive pattern, and affects an estimated 1.6 to 6 in 1 million children, and is responsible for less than 10 percent of all cases of long QT syndrome. Like long QT syndrome, Jervell and Lange-Nielsen syndrome is a heart condition that causes the cardiac muscle to take longer than usual to recharge between beats. I ...